Paper Type |
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Research Paper |
Title |
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Oral rehabilitation of two siblings with Ectodermal Dysplasia a case report |
Country |
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India |
Authors |
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Dr. Amitava Bora , Dr. Abhirup Goswami , Dr. Sudipta Kar, Dr. Gautam Kumar Kundu |
 |
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10.9790/0853-13541218  |
Abstract: Ectodermal dysplasia (ED) is a congenital syndrome characterised mainly by abnormalities of two or more tissues of ectodermal origin namely skin, nails, hair and teeth. Two brothers of 14 years and 10 years of age respectively reported with chief complaint of multiple missing teeth. Thorough medical and dental examinations were performed and findings were in accordance with the typical features of Ectodermal Dysplasia. Pedigree analysis, dermatoglyphic analysis and skin biopsy were also performed. The elder brother was treated with a maxillary removable overdenture and a mandibular removable partial denture. In the younger brother aesthetic composite restoration was done in maxillary anteriors followed by placement of maxillary and mandibular removable partial dentures.
Key words: Ectodermal Dysplasia, Oligodontia, Prosthesis.
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