Abstract: Neurofibromatosis type 2 (NF2) is a rare genetic autosomal dominant disorder, Its sign is the presence of bilateral vestibular schwannomas with multiple spine tumors. Ependymomas account for more than 75% of intramedullary spinal cord are usually low-grade and especially located in the lower cervical and upper thoracic spine, however, anaplastic ependymomas of spine appear to be very rarely. We report a case of a young female patient with spinal multiple tumors associated with bilateral vestibular schwannomas attribute features of NF2, underwent surgical treatment, whose histologic exam showed anaplastic ependymoma. Our objectif through this case is to demonstrate clinic and radiologic findings, and discuss about histologically features.
Keywords : Spine, Anaplastic, Ependymomas, Neurofibromatosis
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